Benign Familial Pemphigus (Hailey Hailey Disease)

Benign Familial Pemphigus (Hailey Hailey Disease) Definition: Benign familial pemphigus (BFP), also known as “Hailey- Hailey Disease”  is a rare autosomal dominant blistering dermatosis that was discovered in 1939. Etiology: BPH is a hereditary skin disorder caused by variations or mutations in the ATP2C1 gene. This gene is found on chromosome 3q21-24 and is responsible […]

Benign Familial Pemphigus (Hailey Hailey Disease)

Benign Familial Pemphigus (Hailey Hailey Disease) Definition: Benign familial pemphigus (BFP), also known as “Hailey- Hailey Disease”  is a rare autosomal dominant blistering dermatosis that was discovered in 1939. Etiology: BPH is a hereditary skin disorder caused by variations or mutations in the ATP2C1 gene. This gene is found on chromosome 3q21-24 and is responsible […]

Benign Familial Pemphigus (Hailey Hailey Disease)

Benign Familial Pemphigus (Hailey Hailey Disease) Definition: Benign familial pemphigus (BFP), also known as “Hailey- Hailey Disease”  is a rare autosomal dominant blistering dermatosis that was discovered in 1939. Etiology: BPH is a hereditary skin disorder caused by variations or mutations in the ATP2C1 gene. This gene is found on chromosome 3q21-24 and is responsible […]

Benign Familial Pemphigus (Hailey Hailey Disease)

Benign Familial Pemphigus (Hailey Hailey Disease) Definition: Benign familial pemphigus (BFP), also known as “Hailey- Hailey Disease”  is a rare autosomal dominant blistering dermatosis that was discovered in 1939. Etiology: BPH is a hereditary skin disorder caused by variations or mutations in the ATP2C1 gene. This gene is found on chromosome 3q21-24 and is responsible […]